RT Journal Article
SR Electronic
T1 Massive Hemothorax in a Beta-Thalassemic Patient Due to Spontaneous Rupture of Extramedullary Hematopoietic Masses: Diagnosis and Successful Treatment
JF Respiratory Care
FD American Association for Respiratory Care
SP 272
OP 276
VO 51
IS 3
A1 Pornsuriyasak, Prapaporn
A1 Suwatanapongched, Thitiporn
A1 Wangsuppasawad, Narathip
A1 Ngodngamthaweesuk, Montian
A1 Angchaisuksiri, Pantep
YR 2006
UL http://rc.rcjournal.com/content/51/3/272.abstract
AB Intrathoracic extramedullary hematopoiesis is an unusual but well-described entity. The condition is typically found in patients who have chronic hemolytic anemias, especially thalassemia. We report a case of a 38-year-old man with underlying beta thalassemia/hemoglobin E who developed intrathoracic extramedullary hematopoiesis. The hematopoietic masses spontaneously ruptured, resulting in massive hemothorax. The condition was confirmed by video-assisted thoracoscopy and successfully treated with surgery, hydroxyurea, and radiation.