RT Journal Article SR Electronic T1 Lung Transplantation for Williams-Campbell Syndrome With a Probable Familial Association JF Respiratory Care FD American Association for Respiratory Care SP 1505 OP 1508 DO 10.4187/respcare.01484 VO 57 IS 9 A1 S Rodrigo Burguete A1 Stephanie M Levine A1 Marcos I Restrepo A1 Luis F Angel A1 Deborah J Levine A1 Jacqueline J Coalson A1 Jay I Peters YR 2012 UL http://rc.rcjournal.com/content/57/9/1505.abstract AB Williams-Campbell syndrome is a rare disorder characterized by deficiency of subsegmental bronchial cartilage and development of airway collapse and bronchiectasis that may subsequently progress to respiratory failure and death. There are only 2 published reports suggesting a familial association, and only one report of lung transplantation being used as a therapeutic modality. Due to postoperative airway complications, transplantation has not been recommended for this disease. We report the first lung transplant with prolonged survival, approaching 10 years, in a patient with Williams-Campbell syndrome, and provide further evidence to support a familial association.