Original articlePediatric cardiacTracheal Reconstruction in Children With Unilateral Lung Agenesis or Severe Hypoplasia
Section snippets
Material and Methods
This study was approved by the Institutional Review Board (IRB) of Children's Memorial Hospital as a retrospective chart analysis; requirement for consent was waived. Patients with tracheal stenosis were divided into two groups based on their pulmonary anatomy of one lung (SL = unilateral lung agenesis or severe hypoplasia) or two lungs (BL = bilateral lungs).
The two groups were then analyzed for differences in presentation and outcomes. Factors analyzed included preoperative intubation,
Results
Seventy-one patients underwent repair of tracheal stenosis secondary to complete congenital tracheal rings at Children's Memorial Hospital between 1982 and 2008. The SL group had 11 patients; 9 of these patients had absence of the right lung (4) or severe hypoplasia of the right lung (5) (Fig 1). The left lung was absent in 2 patients (Fig 2). The clinical characteristics of these patients are summarized in Table 1. Chest X-ray, axial computed tomographic (CT) image, and three-dimensional (3D)
Comment
In our overall series of 71 patients with tracheal stenosis secondary to complete tracheal rings, 15% had unilateral lung agenesis or severe lung hypoplasia. The purpose of this review was to compare the group of patients with tracheal stenosis and “one lung” with those who had tracheal stenosis and two lungs. We attempted to identify any trends with associated pathology and to evaluate and compare the outcomes of these two groups. One of the earliest reports of unilateral lung agenesis was
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