Background Mutations in the cystic fibrosis transmembrane conductance regulator (CFTR)
gene containing a premature termination signal cause a deficiency or absence of functional …

Objectives: Treatment with pancreatic enzymes fails to completely correct malabsorption and
gastrointestinal symptoms in patients with cystic fibrosis (CF). The aim of the present study …

This 2-year cross-sectional evaluation of nontuberculous mycobacterial (NTM) infections
involved all Israeli medical centers that treat cystic fibrosis patients. The study comprised 186 …

At birth, lung fluid produced during fetal life must be cleared immediately and efficiently
before the first breath takes place, in order for infants to achieve a normal and successful …

Background Respiratory syncytial virus (RSV) is the most common cause of severe lower
respiratory tract infection, with a high global health burden. There are no effective treatments …

… e , Aviv Goldbart MD f , Rina Katz MSc c d e , Yedidia Bentur MD b d e , Lea Bentur MD a d e
… Author contributions: Drs Hakim and L. Bentur both had full access to the data and both will …

The aim of this study was to compare the response to inhaled albuterol after administration
by nebulizer with the response after administration by a metered-dose inhaler and spacer …

Primary ciliary dyskinesia (PCD) is a recessively inherited disease that leads to chronic
respiratory disorders owing to impaired mucociliary clearance. Conventional transmission …

Objective. The aim of this study was to define the role of possible risk factors for the development
of cystic fibrosis (CF)-related liver disease and to analyze the association between liver …

… All doses were suspended in 3 ml of 0.9% saline solution and delivered for 15 minutes
by face mask and nebulizer, which was driven by oxygen at a flow rate of 6 to 7 L/min. …