BACKGROUND: Emphysema, especially in the upper lobes, is frequently observed in association
with idiopathic pulmonary fibrosis (IPF). However, the combination of emphysema plus …

Rationale: The three previously reported cases of conclusively documented pulmonary
lymphangioleiomyomatosis (LAM) in men were associated with definite or probable tuberous …

Respiratory failure has been described in myotonic dystrophy; it worsens during sleep but
its central or peripheral origin has yet to be determined. Moreover, patients may present …

Background: Exertional dyspnea and exercise incapacity are the most prominent and
disabling symptoms and the main contributors to health-related quality of life in patients with …

Patients with severe COPD may be in a state of ventilatory muscle (VM) fatigue. In these
patients, rapid and shallow breathing has been hypothesized to be a compensatory mechanism …

Objectives In the present study, conducted on a relatively large population for a rare disease,
we sought to show the hormonal manipulation's positive effects for the survival rate. …

Objective: The role of active inflammation in idiopathic pulmonary fibrosis (IPF) is controversial.
A gallium‐67 citrate (Ga 67 scan) is a sensitive indicator of inflammatory activity. The aim …

When hypoxemia persists in patients who have had treatment aimed at optimizing ventilation
and in-trapulmonary gas exchange, consideration is given to the use of prolonged oxygen …

The contribution of bullous emphysema (BE) to the functional impairment of patients with
concomitant diffuse emphysema (DE) and the confounding effects of BE on functional …

Aims : To describe two cases of a peculiar pulmonary lesion, which expand both the
morphological and the immunophenotypic spectrum of perivascular epithelioid cell (PEC)‐related …