This document is an international evidence-based guideline on the diagnosis and management
of idiopathic pulmonary fibrosis, and is a collaborative effort of the American Thoracic …

The natural history of idiopathic pulmonary fibrosis (IPF) has been characterized as a steady,
predictable decline in lung function over time. Recent evidence suggests that some …

Acute exacerbation of idiopathic pulmonary fibrosis has been defined as an acute, clinically
significant, respiratory deterioration of unidentifiable cause. The objective of this …

We treated three patients with idiopathic pulmonary fibrosis who had an acute clinical
exacerbation. We analyzed their clinical, radiographic, therapeutic, and pathologic findings. Their …

Background and objective: Although pulmonary rehabilitation is effective for patients with
COPD, its efficacy in patients with IPF is unknown. The purpose of this study was to evaluate …

Rationale: Patients with a clinicopathological diagnosis of idiopathic pulmonary fibrosis (IPF)
may have typical findings of usual interstitial pneumonia (UIP) on computed tomography (…

Rationale: Idiopathic pulmonary fibrosis is a progressive, uniformly fatal interstitial lung disease.
An acute exacerbation of idiopathic pulmonary fibrosis is an episode of acute respiratory …

Background: The impact of pulmonary hypertension (PH) on survival has been
demonstrated in severe cases with idiopathic pulmonary fibrosis (IPF) who were referred for …

This study compared high-resolution computed tomography (CT) findings between 10
survivors and 21 nonsurvivors of acute interstitial pneumonia and evaluated whether the CT …

A randomised, double-blind, phase II, dose escalation trial was conducted to assess the
safety, tolerability and pharmacokinetics of the tyrosine kinase inhibitor nintedanib, alone and …