This study evaluated compliance with non-invasive ventilation in patients with myotonic
dystrophy type 1 and identified predictors of cessation at 5 years in a cohort of patients followed …

Few studies have assessed the impact of home ventilation in patients with myotonic dystrophy
type 1 (DM1) and no specific recommendations are available. We assessed the survival …

Objective To study the ability of peak cough flow (PCF) and effective cough volume, defined
as the volume exsufflated >3 L/s, to detect upper airway collapse during mechanical …

… Author links open overlay panel Ghilas Boussaïd a b d , Frédéric Lofaso b d f , Dante
Brasil Santos b d f , Isabelle Vaugier a d , Sandra Pottier a d , Hélène Prigent b d f , Stéphane …

New treatments are being developed for myotonic dystrophy type 1 (DM1). To evaluate their
efficacy, knowledge about the natural history of respiratory dysfunction and its relationship …

BACKGROUND: Mechanical insufflation-exsufflation (MI-E) devices are used to improve
airway clearance in individuals with acute respiratory failure. Some MI-E devices measure …

BACKGROUND: Duchenne muscular dystrophy (DMD) is a sex-linked genetic disorder in
which progressive impairment of skeletal muscle function eventually leads to severe …

BACKGROUND: The life expectancy of individuals with Duchenne muscular dystrophy has
improved considerably with the use of mechanical ventilation to manage respiratory …

BACKGROUND: Noninvasive ventilation (NIV) is the reference standard treatment for most
situations of chronic respiratory failure. NIV settings must be titrated to both preserve upper-…

Introduction The effect of anti-infective agents in COVID-19 is unclear. The impact of
changes in practice on prognosis over time has not been evaluated. Methods Single center, …