RT Journal Article
SR Electronic
T1 Massive Intractable Hemoptysis Due to Idiopathic Granulomatous Pulmonary Veno-occlusive Disease
JF Respiratory Care
FD American Association for Respiratory Care
SP e56
OP e59
DO 10.4187/respcare.02084
VO 58
IS 5
A1 T Eoin West
A1 C Dirk Keene
A1 Rodney A Schmidt
A1 Kelly D Smith
YR 2013
UL http://rc.rcjournal.com/content/58/5/e56.abstract
AB Pulmonary veno-occlusive disease is a rare condition with limited treatment options. The pathological hallmark of the disease is occlusion of pulmonary venules and small veins in the lobular septa. The etiology of the disease remains obscure. We report and discuss an extremely unusual case presenting as massive and intractable hemoptysis, in which pulmonary venous occlusion was attributed to granulomatous venulitis in the absence of other pulmonary or systemic inflammatory abnormalities.