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Causes of congenital unilateral pulmonary hypoplasia: a study of 33 cases

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Abstract

A review of the roentgenograms and clinical records of 33 children with primary congenital underdevelopment of one lung showed that 9 patients had simple pulmonary hypoplasia, 8 had anomalous venous return to the right atrium or the inferior vena cava (scimitar syndrome), 7 had an absence of the ipsilateral pulmonary artery, 7 had an accessory diaphragm, and 2 had a pulmonary sequestration adjacent to a small diaphragmatic hernia.

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Authors and Affiliations

  1. Department of Radiology, Children's Medical Center and the University of Texas, Southwestern Medical School, Dallas, Texas, USA

    G. Currarino & B. Williams

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  1. G. Currarino
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  2. B. Williams
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Currarino, G., Williams, B. Causes of congenital unilateral pulmonary hypoplasia: a study of 33 cases. Pediatr Radiol 15, 15–24 (1985). https://doi.org/10.1007/BF02387847

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  • DOI: https://doi.org/10.1007/BF02387847

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