Chest
Sjögren's Syndrome with Multiple Bullae and Pulmonary Nodular Amyloidosis
Section snippets
CASE REPORT
A 53-year-old woman was admitted to our hospital with the chief complaints of cough and exertional dyspnea, which had appeared three years earlier and had steadily progressed. Multiple linear shadows and bullous change were presented on chest roentgenograms six years ago, but at that time, she did not have any pulmonary complaint. She also complained of dryness of the conjunctiva and mouth. The physical examination disclosed only slight crepitations on chest auscultation. Laboratory examination
DISCUSSION
Although pulmonary complications associated with Sjögren's syndrome have attracted attention in recent years,1, 2 bullae formation has been reported in only one case;3 pulmonary nodular amyloidosis is also a rare concomitant.1, 3 Thus, this is the first report of a patient having these two complications.
In this patient, the primary and most interesting change was the infiltration of lymphocytes and plasma cells into the bronchiolar wall, without involvement of other lung regions. Extensive
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