Noninvasive ventilation during gastrostomy tube placement in patients with severe duchenne muscular dystrophy: case reports and review of the literature

Pediatr Pulmonol. 2006 Feb;41(2):188-93. doi: 10.1002/ppul.20356.

Abstract

Individuals with Duchenne muscular dystrophy may benefit from gastrostomy tube feeding due to progressive dysphagia and malnutrition. However, due to their severely impaired pulmonary function, these individuals are at risk of severe complications when they are sedated or undergo anesthesia for the procedure. We previously described a technique of noninvasive positive pressure ventilation to provide respiratory support during gastrostomy tube placement in such patients, but this technique had risks and limitations. In this case report, we examine two alternative techniques we used to provide respiratory support successfully to patients with severe muscular dystrophy and malnutrition who underwent percutaneous endoscopic gastrostomy tube placement. We then review the literature and discuss the potential benefits, risks, and limitations of the above techniques and of other options for gastrostomy placement in people with severe muscular dystrophy.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Follow-Up Studies
  • Gastrostomy*
  • Humans
  • Laryngeal Masks
  • Male
  • Muscular Dystrophy, Duchenne / therapy*
  • Positive-Pressure Respiration / methods*
  • Retrospective Studies
  • Severity of Illness Index