Abstract
Patients with Fontan palliation and single-ventricle physiology encounter multiple comorbidities including plastic bronchitis, a disease characterised by the plugging of small and large airways by rubbery, white casts. To date, no controlled clinical trials have demonstrated effective treatment of plastic bronchitis. We report the application of aerosolised heparin, which has published success in non-cardiac-related pulmonary disease, for this complication in a Fontan patient.
MeSH terms
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Administration, Inhalation
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Aerosols
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Bronchitis / complications
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Bronchitis / drug therapy*
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Child, Preschool
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Female
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Fibrinolytic Agents / therapeutic use*
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Fontan Procedure*
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Heart Septal Defects, Ventricular / complications
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Heart Septal Defects, Ventricular / surgery*
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Heart Ventricles / abnormalities
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Heart Ventricles / surgery*
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Heparin / therapeutic use*
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Humans
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Pulmonary Valve Stenosis / complications
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Pulmonary Valve Stenosis / surgery*
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Treatment Outcome
Substances
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Aerosols
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Fibrinolytic Agents
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Heparin